Pulmonary hypertension diagnosed by echocardiography during idiopathic myelofibrosis

A case report and a brief review of the literature

  • Claudio Perrone | claudiolvperrone@libero.it Respiratory Function Unit, ASL Viterbo, Presidio Ospedaliero Centrale “Belcolle”, Viterbo, Italy.
  • Roberto Cartolari 1Respiratory Function Unit, ASL Viterbo, Presidio Ospedaliero Centrale “Belcolle”, Viterbo, Italy.
  • Beatrice Lupi Department of Internal Medicine, Policlinico Umberto I, University "Sapienza", Rome, Italy.
  • Sergio Morelli Department of Internal Medicine, Policlinico Umberto I, University "Sapienza", Rome, Italy.

Abstract

Idiopathic myelofibrosis is a rare chronic myeloproliferative disease leading to extramedullary hematopoiesis (myeloid metaplasia) with splenomegaly. The liver and less frequently other organs including the lung can be involved, therefore portal hypertension is relatively common. Pulmonary hypertension (PH) is only occasionally reported, although recent studies have suggested an association between PH and myeloproliferative disorders. We present a case of PH diagnosis by echocardiography in a patient affected by idiopathic myelofibrosis with portal hypertension.

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Published
2010-07-06
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Issue
Section
Case Reports
Keywords:
Asthma, Pregnancy
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How to Cite
Perrone, C., Cartolari, R., Lupi, B., & Morelli, S. (2010). Pulmonary hypertension diagnosed by echocardiography during idiopathic myelofibrosis: A case report and a brief review of the literature. Multidisciplinary Respiratory Medicine, 5(1). https://doi.org/10.4081/mrm.2010.553